Rate of progression of lung function impairment in 1-antitrypsin deficiency
نویسندگان
چکیده
منابع مشابه
Rate of progression of lung function impairment in alpha1-antitrypsin deficiency.
The aim of the present study was to identify alpha(1)-antitrypsin (alpha(1)-AT)-deficient patients who had rapidly progressive disease. PiZ patients (n = 101) underwent annual lung function measurements over a 3-yr period, and the results were related to factors that may influence decline. The mean annual decline in forced expiratory volume in 1 s (FEV(1)) was 49.9 mL. The greatest FEV(1) decli...
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ژورنال
عنوان ژورنال: European Respiratory Journal
سال: 2009
ISSN: 0903-1936,1399-3003
DOI: 10.1183/09031936.00061208